Table 2 Imaging and treatment characteristics of 13 BHD patients with (recurrent) SP after air travel
Patient number | Thoracic CT Available | Number of cysts | Prior SP | Prior pleurodesis | Treatment SP after air travel | FLCN mutation |
|---|---|---|---|---|---|---|
1 | Yes | 5 | Yes | Yes | Pleurodesis | c.610_611delinsTA |
2 | Yes | 1 | Yes | No | Pleurodesis | c.499C>T |
3 | n/a | n/a | Yes | No | Pleurectomy/pleurodesis | c.250-?_1740+?del (del exon 5–14) |
4 | Yes | 99 | No | No | Tube thoracostomy | c.1285dupC |
5 | Yes | 140 | No | No | Tube thoracostomy | c.1408_1418del; p.Gly470fs |
5 | Yes | 140 | Yes | Yes | Pleurodesis | c.1408_1418del; p.Gly470fs |
6 | Yes | 4 | Yes | No | Pleurodesis | c.619-1G>A |
7 | n/a | n/a | Yes | No | Tube thoracostomy | c.1539-2A>G |
8 | Yes | 74 | No | No | Pleurodesis | c.1539-2A>G |
9 | n/a | n/a | Yes | No | Pleural rubbing | c.610_611delinsTA |
10 | Yes | 19 | Yes | Yes | Pleurodesis | c.610_611delinsTA |
11 | n/a | n/a | Yes | No | Pleural rubbing | c.1065_1066delGCinsTA |
12 | n/a | n/a | No | No | Tube thoracostomy | c.610_611delinsTA |
13 | Yes | 99 | No | No | Tube thoracostomy | c.1740dupC |
13 | Yes | 99 | Yes | No | Apical pleurectomy | c.1740dupC |
13 | Yes | 99 | Yes | No | Total pleurectomy and pleurodesis | c.1740dupC |