From: Mutation spectrum of Egyptian children with cystic fibrosis
Variables | N = 60 (%) |
---|---|
Age (years)a | 5 (0.5–14) |
Gender | |
Male | 38 (63) |
Female | 22 (37) |
Positive family history of CF | 14 (23) |
Positive consanguinity | 34 (57) |
Clinical presentations | |
Pulmonary disease | 56 (93) |
Pancreatic insufficiency | 52 (87) |
Hepatic disease | 9 (15) |
Intestinal obstruction | 2 (3) |
Nasal polyps | 13 (22) |
Sinusitis | 13 (22) |
Pseudo barter | 1 (1.66) |