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Table 3 Frequency of different clinical features in MRH reported

From: Multicentric reticulohistiocytosis (MRH): case report with review of literature between 1991 and 2014 with in depth analysis of various treatment regimens and outcomes

Clinical features

n = 52

Arthritis

43

Erosive disease

23

Arthralgia

5

Arthritis mutilans

4

Tenosynovitis

3

Skin lesions

50

Pseudoptosis

1

Weight loss

10

Weakness

8

Dysphagia

5

Fatigue

5

Fever

5

Nodules on epiglottis

3

Hoarseness

3

Sicca

3

Nodules in larynx

2

Muscle atrophy

2

Myalgia

2

Mucosal lesions

2

Macroglossia

1

Parotid enlargement

1

URI symptoms

1

PPD+

1

Lymphadenopathy

1

Raynaud’s phenomenon

1

Splenomegaly

1