Acute adult-onset still’s disease presenting as pulmonary hemorrhage, urticaria, angioedema and leukemoid reaction: a case report and literature review

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Table 1 Summary of the differential diagnosis of urticaria, arthritis and fever from the literature

Classes of diseases	Diseases
Hereditary auto-inflammatory syndromes	Familial cold urticaria
	Cryopyrin-associated syndrome
	Muckle–Wells syndrome
	Familial cold urticaria
	Chronic infantile neurologic cutaneous and
	articular syndrome (CINCA/NOMID)
Infectious diseases	Hepatitis B, C
	Chronic meningococcemia
	STAR complex (Sore Throat, Arthritis and Rash secondary to a viral infection)
	Streptococcal pharyngitis with reactive arthralgia and exanthem
Autoimmune disorders	AOSD
	Systemic lupus erythematosus
	Acquired C1 esterase deficiency
	Schnitzler syndrome
Hematological disorders	Lymphoma
	Monoclonal gammopathy of unknown significance
	Multiple myeloma
	Polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS) syndromeº
	Waldenström’s macroglobulinemia
Other	Hypocomplementic urticarial vasculitis
	Idiopathic chronic urticaria
	Delayed pressure urticaria
	Cryoglobulinemia
	Behçet’s disease
	Mastocytosis

Modificated and update from: (Affleck and Littlewood 2005; Koning et al. 2007; Kyle and Rajkumar 2003; Csepregi and Nemesánszky 2000; Davis and Brewer 2004; Hawkins et al. 2004; Tomkova et al. 1998; Zuberbier et al. 2009; Deacock 2008).