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Table 1 Case reports published describing an overlap between ANCA associated vasculitis and rheumatoid arthritis

From: Association of ANCA associated vasculitis and rheumatoid arthritis: a lesser recognized overlap syndrome

Year/Cases

Diagnoses

Age RA

Age VAS

Vasculitis symptoms

Positive antibodies

RA therapy

Follow-up

1974/1 (Pritchard 1976)

RA/GPA

40

59

ENT

RhF, ANA

Gold, tuberculin injections, NSAID

D

1976/2 (Ohashi et al. 1992)

RA/GPA

45

45

ENT

RhF

HCQ, aspirin

I

RA/GPA

73

75

ENT, Eyes, Lung

RhF

Gold, NSAID

I

11992/1 (Steuer et al. 1995)

RA/GPA

33

38

ENT

RhF

NSAID, Gold

I

1995/1 (Harper et al. 1997)

RA/MPA

49

62

Lung,Kidney

RhF, ANA, p-ANCA

NSAID, Gold, SFZ

I

1997/10 (Messiaen et al. 1998)

RA/MPA

31-62

NA

5: kidney only

4: p-ANCA

6: NSAID

4 D

1: kidney, lung, eye

9: RhF

1: NSAID, Penicillamine HCQ

2 HD

3: kidney, skin

6: ANA

1: Prednisone, SFZ, Gold

4 I

1:kidney, bowel, skin

1: HCQ

1: HCQ, SFZ

1999/1 (Yorioka et al. 1999)

RA/MPA

22

24

Kidney

RhF, ANA, MPO-ANCA

NSAID

I

2002/2 (Chinoy & McKenna 2002)

RA/GPA

32

32

ENT, Lung, Kidney

p-ANCA

Prednisolone, NSAID, CYC

I

RA/GPA

*41

26

Lung

p-ANCA

I

2003/2 (Douglas et al. 2003)

RA/GPA

36

37

ORL, Lung, Kidney

RhF, PR3-ANCA

Prednisolone, MTX, NSAID.

I

RA/GPA

35

55

Lung

RhF, PR3-ANCA

NSAID, MTX

I

2005/1 (Goto et al. 2005)

RA/MPA

44

48

ORL, eyes, Kidney

MPO-ANCA, RhF, ANA

MTX, Penicillamine, Gold, prednisolone

I

2008/1 (Pai & Panda 2008)

RA/GPA

57

60

Lung

RhF, Anti-CCP, PR3-ANCA

HCQ, prednisolone

I

2012/4 (Szilasi et al. 2012)

RA/GPA

40

70

Lung, Kidney

PR3-ANCA, Anti-CCP,RhF

Prednisolone

I

RA/MPA

*49

44

Lung, Kidney

MPO-ANCA, RhF

Adalimumab, RTX

I

RA/MPA

28

34

Lung, Kidney

MPO-ANCA, RhF

Prednisone, SFZ, MTX

I

RA/EGPA

52

54

Skin

MPO-ANCA, RhF

MTX, Cyclosporine

I

2012/1 (Vaishnav et al. 2012)

RA/GPA

36

37

Lung

c-ANCA, RhF

 

D

2013/1 (Reitblat & Reitblat 2013)

RA/GPA

45

58

Kidney

PR3-ANCA, RhF

MTX, Etanercept

HD

2014/1 (Ortiz-Sierra et al. 2014)

RA/GPA

65

67

Skin, lung, ENT, eye

RhF, c-ANCA

MTX, Prednisone, etanercept,

I

Our report

5 RA/MPA

24-63

63-69

1: Kidney, lung

3: RhF

1: MTX, prednisone

5 I

1 RA/GPA

5: Kidney

1: Anti-CCP

1: SFZ

1 HD

1: PR3-ANCA

1: HCQ, MTX, leflunomide

1D

3: MPO-ANCA

1: Infliximab, MTX, SFZ

1: Etanercept, MTX, SFZ, AZA

1: Prednisolone

  1. RA: Rheumatoid Arthritis, GPA: Granulomatosis with polyangiitis, MPA: Microscopic polyangiitis, EGPA (Churg-Strauss Syndrome), ENT: ear, nose and throat; HCQ: hydroxychloroquine, NSAID: non-steroidal anti-inflammatory drug, CP: cyclophophamide; AZA: Azathioprine, SFZ: sulfasalazine, MTX: methotrexate, D: dead, I: AAV improved, HD: Hemodialysis.