• | Atypical attacks duration [Mani & Deeter 1982, West & Todman 1991, Todo & Inoya 1991, Zanchin et al. 1995, Milos et al. 1996, Mainardi et al. 2002, Razvi et al. 2006, Park et al. 2006, Massie et al. 2006, Favier et al. 2007a case 2, Rigamonti et al. 2007 case 1, Hardmeier et al. 2007, Cologno et al. 2008, Tobin & Flitman 2008, Eimil-Ortiz et al. 2008, Robbins et al. 2009, Liu & Su 2009* |
• | Atypical attack frequency [Todo & Inoya 1991, Favier et al. 2007a case 2 and 3, Alty et al. 2008, Eimil-Ortiz et al. 2008 |
• | Atypical attack duration and frequency [Todo & Inoya 1991, Favier et al. 2007a case 2, Eimil-Ortiz et al. 2008 |
• | Atypical attack duration and abnormal findings on neurologic examination [Mainardi et al. 2002, Razvi et al. 2006, Park et al. 2006, Massie et al. 2006, Favier et al. 2007a case 2, Rigamonti et al. 2007 case 1, Hardmeier et al. 2007, Tobin & Flitman 2008, Liu & Su 2009 |
• | Did not meet the criterion of five attacks [Todo & Inoya 1991 |
• | Continuous headache or a background headache [Hannerz 1989, West & Todman 1991, Todo & Inoya 1991, Taub et al. 1995, Frigerio et al. 2003, Favier et al. 2007a case 3, Hardmeier et al. 2007, Kim et al. 2008, Harley & Ahmed 2008 |
• Atypical symptoms: |  |
 | Impotence [Tfelt-Hansen et al. 1982 |
 | Symptoms of acromegaly [Milos et al. 1996 |
 | Episodes of altered consciousness [Munoz et al. 1996 case 2, Favier et al. 2007a: case 2] |
 | Headache triggered by sitting or standing [Piovesan et al. 2001 |
 | and purulent nasal discharge [Scorticati et al. 2002 |
 | Acute weakness in the upper extremity [Liu & Su 2009 |
• Physical abnormalities on clinical examination: |  |
 | Testicular atrophy [Tfelt-Hansen et al. 1982 |
 | Ophthalmoplegia [Hannerz 1989, Todo & Inoya 1991, Taub et al. 1995, Mainardi et al. 2002, Frigerio et al. 2003, Hannerz et al. 2005, Razvi et al. 2006, Park et al. 2006, Favier et al. 2007a: case 2: Favier et al. 2007b, Rigamonti et al. 2007 case 1 and 2, Hardmeier et al. 2007, Straube et al. 2007 case 2, Valença et al. 2007 case 1 and 2, Godeiro-Junior et al. 2008, Tobin & Flitman 2008, Ashkenazi & Brown 2008 |
 | Optic atrophy [Tfelt-Hansen et al. 1982 |
 | Papilloedema [Park et al. 2006 |
 | Bitemporal hemianopia [Favier et al. 2007b |
 | Adie syndrome [Favier et al. 2007a: case 2] |
 | Persistent partial or complete Horner syndrome [Mainardi et al. 2002, Frigerio et al. 2003, Hannerz et al. 2005, Razvi et al. 2006 Rigamonti et al. 2007 case 1 and 2, Hardmeier et al. 2007, Straube et al. 2007 case 2, Godeiro-Junior et al. 2008, Tobin & Flitman 2008 |
 | Signs of acromegaly [Milos et al. 1996 |
 | Absent radial pulse [Piovesan et al. 2001 |
 | Trigeminal distribution numbness [Massie et al. 2006, Gentile et al. 2007, Ashkenazi & Brown 2008, Alty et al. 2008, Liu & Su 2009 |
 | Swelling of the eye [Favier et al. 2007a: case 3, Ashkenazi & Brown 2008, Kim et al. 2008 |
 | Absent nasal tickle reflex [Massie et al. 2006 |
 | Purulent nasal discharge [Scorticati et al. 2002 |