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Table 1 Etiologies of superior vena cava syndrome

From: Review of evolving etiologies, implications and treatment strategies for the superior vena cava syndrome

Etiology (Rice et al. 2006a; Chen et al. 1990; Mineo et al. 1999; Schraufnagel et al. 1981; Nicholson et al. 1997; Hohloch et al. 2014; Lonardi et al. 2002)

Prevalence (%) (Rice et al. 2006a; Chen et al. 1990; Mineo et al. 1999; Schraufnagel et al. 1981; Nicholson et al. 1997; Hohloch et al. 2014; Lonardi et al. 2002)

Malignant

Non-small cell lung cancer

22–57

Small cell lung cancer

10–39

Lymphoma

1–27

“Other metastasis”

19

Other adenocarcinoma

3–15

Germ cell tumors

2–6

Thymoma

1–3

Sarcomas

2

Esophageal carcinoma

2

AML

1

Tuberculosis lymphangitis

2

Benign

Port-a-cath

16

Dialysis catheter

5

Fibrosing mediastinitis

2–9

Mesothelioma

1–7

Mustard operation

5

Primary SVC thrombosis

1–5

Retrosternal goiter

3

Tuberculosis lymphangitis

2

Behcet’s syndrome

2

Pacemaker wire

1–2

Hematoma after aortic dissection repair

1

Pseudotumor

1

Hickman catheter

1

Aneurysm

1

Radiation fibrosis

1

  1. Malignant and non-malignant causes of superior vena cava syndrome